Distal intestinal obstruction syndrome in a patient with cystic fibrosis after lung transplantation

Abstract

Distal intestinal obstruction syndrome (DIOS) belongs to intestinal complications of cystic fibrosis (CF). It is characterized by complete or incomplete obstruction of the intestine with inspissated intestinal contents, most frequently in the terminal ileum, caecum and ascending colon. The most common clinical manifestation is crampy abdominal pain, generally located in the right lower quadrant, with a palpable mass of replete bowels and vomiting. Computer tomography scan (CT) can differentiate DIOS from other painful disorders in the right hypogastrium. Patients with incomplete DIOS usually respond to oral rehydration and osmotic laxatives. Those with complete DIOS should be treated from below with hyperosmolar contrast enemas. Patients with signs of peritonitis may require surgical treatment. We present our experience with DIOS on the following case report.